Although all disorders underlying horner syndrome may potentially present as pdps, very few cases of the latter have been described in the literature. Pourfour du petit syndrome in a patient with thyroid carcinoma. Claude bernardhorner syndrome as a rare complication of. In rare cases, horner s syndrome is congenital present from birth and may be associated with a lack of pigmentation of the iris colored part of the eye. Horner syndrome horner s syndrome results from an interruption of the sympathetic nerve supply to the eye and is characterized by the classic triad of miosis ie, constricted pupil, partial. Files are available under licenses specified on their description page. Claude bernard horner syndrome presents various etiologies and occurs as the direct result of interrupted nerve signaling at any point along the nerve trajectory, be it intrathoracic or extrathoracic. A clinical report of the syndrome in a man shot through the throat was rendered in 1864 by the three american army physicians silas weir mitchell 18291914, who had been influenced by bernard. Horner s syndrome, also known as oculosympathetic paresis, is a combination of symptoms that arises when a group of nerves known as the sympathetic trunk is damaged.
View enhanced pdf access article on wiley online library html view download pdf for offline viewing. June 2009 claude bernard horner syndrome as a rare complication of postoperative drainage. Hospital provincial universitario arnaldo milian castro. Puede agregarse adems inyeccin conjuntival ojo rojo. It was more thoroughly described by claude bernard in 1852. The underlying causes of horner s syndrome vary greatly and may include a tumor, stroke, injury, or underlying disease affecting the areas surrounding the sympathetic nerves. Le patient beneficie dune irm cervicothora cique qui. The term horner syndrome is commonly used in englishspeaking countries, whereas the term ber. Horner syndrome horner s syndrome results from an interruption of the sympathetic nerve supply to the eye and is characterized by the classic triad of miosis ie, constricted pupil, partial ptosis, and loss of hemifacial sweating ie, anhidrosis. The clinical presentation of pourfour du petit syndrome pdps is the opposite of horner syndrome. All structured data from the file and property namespaces is available under the creative commons cc0 license. Horners syndrome genetic and rare diseases information. Horner syndrome is a classic neurologic syndrome whose signs include miosis, ptosis, and anhidrosis. Horner syndrome is a neurological disorder affecting the eye in which the eyelids appear drooping and the eye seems sunken.
Statistiche sindrome di bernard horner mappa sindrome. It is characterized by miosis a constricted pupil, partial ptosis a weak, droopy eyelid, apparent anhydrosis decreased. Pdf bernard horner syndrome after accidental lesion of. We report a patient with pdps due to carotid compression by a thyroid tumor. Pablo ioli historia johann friedrich horner 18311886 naci y realiz su prctica mdica en zurich. We present the case of a patient with this unusual presentation. Also called oculosympathetic paresis, a horner syndrome can be produced by a lesion anywhere along the sympathetic pathway that supplies the head, eye, and neck. The content of the website and databases of the national organization for rare disorders nord is ed and may not be reproduced, copied, downloaded or disseminated, in any way, for any commercial or public purpose, without prior written authorization and approval from nord. The association of unilateral trochlear nerve palsy with claude bernardhorner syndrome represents a rare clinical condition. Horners syndrome nord national organization for rare. The signs and symptoms occur on the same side ipsilateral as it is a lesion of the sympathetic trunk. Scribd is the worlds largest social reading and publishing site. The investigation performed implicated cerebrovascular disease as the underlying cause of the condition in this patient. Trochlear nerve palsy associated with claude bernard.
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